THE COMBINATION OF KARTAGENER SYNDROME WITH FOCAL SEGMENTAL GLOMERULOSCLEROSIS: CASE REPORT

  • E.V. Burdeina SI «Institute of Nephrology NAMS of Ukraine»
  • V.N. Nepomnyashchy SI «Institute of Nephrology NAMS of Ukraine»
  • N.A. Kolesnyk SI «Institute of Nephrology NAMS of Ukraine»
Keywords: Kartageners syndrome, primary ciliary dyskinesia, dextrocardia, focal segmental glomerulosclerosis, nephrotic syndrome, situs inversus.

Abstract

Kartagener syndrome - a form ofprima­ry ciliary dyskinesia, which combines situs inversus totalis or only dextrocardia with the defeat of the respiratory sys­tem. The combination of glomerulonephritis with Kartagen­er syndrome is rare, and that was the reason for describing a patient with Kartagener syndrome and focal - segmental glomerulosclerosis observed in clinic.

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Published
2015-11-27
How to Cite
Burdeina, E., Nepomnyashchy, V., & Kolesnyk, N. (2015). THE COMBINATION OF KARTAGENER SYNDROME WITH FOCAL SEGMENTAL GLOMERULOSCLEROSIS: CASE REPORT. Ukrainian Journal of Nephrology and Dialysis, (4(48), 64-68. https://doi.org/10.31450/ukrjnd.4(48).2015.12